Year 2026 / Volume 118 / Number 1
Digestive Diseases Image
Unraveling the mystery: congenital absence of the portal vein and its cardiac implications

43-45

DOI: 10.17235/reed.2024.10323/2024

Zhanwen Xu, Xiaoping Yin,

Abstract
A 25-year-old male with tachycardia and right heart enlargement was diagnosed with atrial-ventricular nodal reentrant tachycardia (AVNRT) and successfully treated with radiofrequency ablation. Cardiac MRI confirmed right heart enlargement but ruled out cardiomyopathy. Further imaging revealed a rare congenital absence of the portal vein (CAPV) with an associated portosystemic shunt. This case highlights the importance of considering CAPV in unexplained cardiac symptoms and structural heart changes.
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References
Baiges A, Turon F, Simón-Talero M, et al. Congenital Extrahepatic Portosystemic Shunts (Abernethy Malformation): An International Observational Study. Hepatology 2020, 71, 658–669.
1. Baiges A, Turon F, Simón-Talero M, TasaycoS, Bueno J,Zekrini K, et al. Congenital Extrahepatic Portosystemic Shunts (Abernethy Malformation): An International Observational Study. Hepatology.2020;71:658–669.
2. Castro Rodríguez J, Rodríguez Perálvarez ML, Montero-Álvarez JL. Diagnosis and management of Abernethy syndrome. Rev Esp Enferm Dig. 2024;116:1-6.
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Xu Z, Yin X. Unraveling the mystery: congenital absence of the portal vein and its cardiac implications. 10323/2024


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Publication history

Received: 04/02/2024

Accepted: 16/02/2024

Online First: 07/03/2024

Published: 14/01/2026

Article Online First time: 32 days

Article editing time: 710 days


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