Año 2017 / Volumen 109 / Número 9
Caso Clínico
Synchronous intraductal papillary mucinous neoplasm and a pancreatic neuroendocrine tumor: more than a coincidence?

663-635

DOI: 10.17235/reed.2017.5003/2017

Juliana M. Costa, Sofia Carvalho, João B. Soares,

Resumen
Background: Although the association between intraductal papillary mucinous neoplasm of the pancreas (IPMN) and pancreatic neuroendocrine tumor (PNET) has been increasingly reported, whether this association is real or coincidence remains unclear. We report a case of synchronous IPMN and a PNET which were diagnosed preoperatively and discuss the tumorigenesis, clinicopathological features and management of these rare tumors based on the published literature. Case report: A 56-year-old male was incidentally diagnosed with a 14 mm branch duct IPMN and a 3.6 mm non-functional PNET during an evaluation due to persistent upper abdominal pain via endoscopic ultrasound. Close follow-up of the patient was decided as the IPMN had no worrisome features. A review of twenty-two previously reported cases of synchronous IPMN and PNET indicated that: a) only seven cases were diagnosed preoperatively; b) abdominal pain was the main presenting symptom; c) IPMN was the dominant tumor and presented with low grade dysplasia; d) the PNET was small and non-functional and had an indolent behavior; and e) only one case underwent radiologic follow-up. Discussion: IPMN are associated with other pancreatic and extrapancreatic malignancies. Thus, the entire pancreatic parenchyma should be examined closely during the evaluation of an IPMN in order to exclude other pancreatic lesions, for example, a PNET.
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Bibliografía
1. Gill KR, Scimeca D, Stauffer J, Krishna M, Woodward TA, Jamil LH, et al. Pancreatic Neuroendocrine Tumors among Patients with Intraductal Papillary Mucinous Neoplasms: Real Association or Just a Coincidence? JOP 2009; 10(5): 515-7.
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Costa J, Carvalho S, Soares J. Synchronous intraductal papillary mucinous neoplasm and a pancreatic neuroendocrine tumor: more than a coincidence? . 5003/2017


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Ficha Técnica

Recibido: 10/04/2017

Aceptado: 17/05/2017

Prepublicado: 14/07/2017

Publicado: 31/08/2017

Tiempo de revisión del artículo: 35 días

Tiempo de prepublicación: 95 días

Tiempo de edición del artículo: 143 días


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