Year 2022 / Volume 114 / Number 12
Letter
Primary intestinal lymphangiectasia: a rare disease as a cause of protein-losing enteropathy

762-763

DOI: 10.17235/reed.2022.8673/2022

Rita González Núñez, Ana Belén Domínguez Carbajo, Laura Alcoba Vega, Jesús Espinel Díez, Santiago Vivas Alegre,

Abstract
Primary intestinal lymphangiectasia is a rare disorder associated with protein-losing enteropathy. The main manifestations are those resulting from hypoalbuminemia. Diagnosis requires the typical endoscopic image of intestinal lymphangiectasia and increased 24-hour fecal alpha-1-antitrypsin clearance. Treatment is basically dietary.
Share Button
New comment
Comments
No comments for this article
References
1.Waldmann TA, Steinfeld JL, Dutcher TF et al. The role of the gastrointestinal system in "idiopathic hypoproteinemia". Gastroenterology 1961 9;41:197-207.
2. Brownell JN, Piccoli D. Protein-losing gastroenteropathy. En Lamont JT, Grover S (Ed.). UpToDate [Internet] [Consultado 2021 diciembre 2]. Disponible en https://www.uptodate.com/contents/protein-losing-gastroenteropathy?search=enteropatia%20pierde%20proteinas&source=search_result&selectedTitle=1~83&usage_type=default&display_rank=1
3.Vignes S. Linfangiectasia intestinal primaria. Orphanet [Internet] [consultado 2021 noviembre 15]. Disponible en: https://www.orpha.net/consor4.01/www/cgi-bin/Disease_Search.php?lng=ES&data_id=12030&Disease_Disease_Search_diseaseGroup=linfangiectasia-intestinal-primaria&Disease_Disease_Search_diseaseType=Pat&Enfermedad(es)/grupo%20de%20enfermedades=Linfangiectasia-intestinal-primaria&title=Linfangiectasia%20intestinal%20primaria&search=Disease_Search_Simple.
4. Wu J, Huang Z, Ji M et al. The diagnostic value of capsule endoscopy in children with intestinal lymphangiectasia. Rev Esp Enferm Dig. 2021 Nov;113(11):765-769.
5. Ingle SB, Hinge (Ingle) CR. Primary intestinal lymphangiectasia: Minireview. World J Clin Cases 2014 16; 2(10): 528-533.
Related articles

Letter

Blue rubber bleb nevus syndrome

DOI: 10.17235/reed.2023.9913/2023

Digestive Diseases Image

Enteroenteric intussusception caused by a small bowel metastatic cutaneous melanoma

DOI: 10.17235/reed.2023.9876/2023

Letter

Capsule endoscopy diagnosis of gastrointestinal melanoma

DOI: 10.17235/reed.2023.9803/2023

Letter

Isolated Jejunal Crohn's Disease: a challenging diagnosis

DOI: 10.17235/reed.2022.9423/2022

Digestive Diseases Image

Whipple’s disease – A typical endoscopic finding of a rare disease

DOI: 10.17235/reed.2022.9338/2022

Letter

Primary intestinal melanoma?

DOI: 10.17235/reed.2022.8944/2022

Digestive Diseases Image

Ileal neuroendocrine tumor as an uncommon cause of obscure gastrointestinal bleeding

DOI: 10.17235/reed.2022.8641/2022

Digestive Diseases Image

Duodenal-type follicular lymphoma: a silent tumor

DOI: 10.17235/reed.2021.8149/2021

Letter

Bochdalek hernia: use of capsule endoscopy

DOI: 10.17235/reed.2021.7760/2020

Review

Advanced therapy by device-assisted enteroscopy

DOI: 10.17235/reed.2020.6971/2020

Digestive Diseases Image

Gastrointestinal and renal involvement in systemic vasculitis

DOI: 10.17235/reed.2020.6965/2020

Editorial

Does it matter how long the small bowel is?

DOI: 10.17235/reed.2020.6980/2020

Digestive Diseases Image

Enteroscopy in the diagnosis of melanoma metastases

DOI: 10.17235/reed.2020.6820/2019

Digestive Diseases Image

Enteroscopic diagnosis of intestinal malabsorption of a rare etiology: diaphragm disease

DOI: 10.17235/reed.2020.6723/2019

Digestive Diseases Image

Jejunal schwannoma detected by video capsule endoscopy

DOI: 10.17235/reed.2020.6474/2019

Digestive Diseases Image

Capsule endoscopy, a useful tool for the diagnosis of a tapeworm infection

DOI: 10.17235/reed.2019.6346/2019

Letter

Use of patency capsule in daily practice

DOI: 10.17235/reed.2019.5952/2018

Digestive Diseases Image

Metastasis of dermatofibrosarcoma diagnosed by capsule endoscopy

DOI: 10.17235/reed.2018.4900/2017

Letter to the Editor

Symptomatic retention of the Agile® patency capsule

DOI: 10.17235/reed.2017.4691/2016

Letter to the Editor

Whipple’s disease under the vision of capsule endoscopy

DOI: 10.17235/reed.2016.4362/2016

Letter to the Editor

Asymptomatic bronchial aspiration of capsule endoscope: a significant complication

DOI: 10.17235/reed.2016.4363/2016

Case Report

Atypical diagnosis diagnosis by endoscopic capsule: Whipple´s disease

DOI: 10.17235/reed.2015.3718/2015

Citation tools
González Núñez R, Domínguez Carbajo A, Alcoba Vega L, Espinel Díez J, Vivas Alegre S. Primary intestinal lymphangiectasia: a rare disease as a cause of protein-losing enteropathy. 8673/2022


Download to a citation manager

Download the citation for this article by clicking on one of the following citation managers:

Metrics
This article has received 1720 visits.
This article has been downloaded 179 times.

Statistics from Dimensions


Statistics from Plum Analytics

Publication history

Received: 02/02/2022

Accepted: 08/02/2022

Online First: 04/03/2022

Published: 12/12/2022

Article Online First time: 30 days

Article editing time: 313 days


Share
This article hasn't been rated yet.
Reader rating:
Valora este artículo:




Asociación Española de Ecografía Digestiva Sociedad Española de Endoscopia Digestiva Sociedad Española de Patología Digestiva
The Spanish Journal of Gastroenterology is the official organ of the Sociedad Española de Patología Digestiva, the Sociedad Española de Endoscopia Digestiva and the Asociación Española de Ecografía Digestiva
Cookie policy Privacy Policy Legal Notice © Copyright 2023 y Creative Commons. The Spanish Journal of Gastroenterology