Year 2024 / Volume 116 / Number 3
Letter
A strange congenital disease, familial megaduodenus: review of the literature

163-164

DOI: 10.17235/reed.2023.9614/2023

Cristina Marco Continente, Pedro Fernández Balaguer, Adrián Hernández Sánchez, Alberto López Farias, Antonio Adolfo Nieto Soler,

Abstract
Familial megaduodenum is an extremely rare congenital disease, with few cases described in the literatura, that is caused by chronic duodenal obstruction of functional type. It presents in the form of nonspecific clinical pseudo-obstruction from infancy, which causes a delay in its diagnosis and treatment. Conservative treatments are rarely sufficient in and of themselves to control the disease, making surgery an effective option in selected patients for relieving or avoiding obstruction, as well as improving duodenal emptying and restoring gastrointestinal tract continuity, paying special attention to the duodenal papilla. We present a case treated at the General Surgery and Digestive Apparatus Service of the Hospital of Mérida and a review of the existing literature.
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References
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Marco Continente C, Fernández Balaguer P, Hernández Sánchez A, López Farias A, Nieto Soler A. A strange congenital disease, familial megaduodenus: review of the literature. 9614/2023


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Publication history

Received: 20/03/2023

Accepted: 28/03/2023

Online First: 19/04/2023

Published: 04/03/2024

Article Online First time: 30 days

Article editing time: 350 days


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